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Amino Acid Metabolism

Amino Acid Metabolism
Transaminase enzymes are present in

none of these
intestine
liver
pancreas

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Amino Acid Metabolism
In the normal breakdown of phenylalanine, it is initially degraded to

fumarate
phenylpuruvate
tyrosine
lysine

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Amino Acid Metabolism
A person with phenylketonuria cannot convert

phenylalanine to isoleucine
phenylalanine to tyrosine
phenol into ketones
phenylalanine to lysine

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Amino Acid Metabolism
A person with phenylketonuria is advised not to consume which of the following products?

Fat containing food
Aspartame
Glycine containing foods
Glucose

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Amino Acid Metabolism
An example of a transamination process is

aspartate + α ketoglutarate = glutamate + oxaloacetate
aspartate + hexanoic acid = glutamate + oxaloacetate
glutamate = α-ketoglutarate + NH3
glutamate = hexanoic acid + NH3

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Amino Acid Metabolism
Oxidative deamination is the conversion of an amino

acid to a keto acid plus ammonia
acid to a carboxylic acid plus ammonia
group from an amino acid to a carboxylic acid
group from an amino acid to a keto acid

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