Amino Acid Metabolism
A person with phenylketonuria cannot convert

phenylalanine to isoleucine
phenylalanine to lysine
phenylalanine to tyrosine
phenol into ketones

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Amino Acid Metabolism
A ketogenic amino acid is one which degrades to

either acetyl CoA or acetoacetyl CoA
pyruvate or citric acid cycle intermediates
keto-sugars
multiple intermediates including pyruvate or citric acid cycle intermediates and acetyl CoA or acetoacetyl CoA

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